En coup de sabre is the other name of Linear scleroderma. In this article we'll be discussing this rare disease, its occurrence, signs and symptoms, pathophysiology, diagnosis and treatment. The special part of this article will be the Ayurvedic management and treatment of this rare ailment. This disease usually affects the children or we can say paediatric patients.
INTRODUCTION
En coup de sabre is also known as linear scleroderma because it covers band-like areas with linear distribution. It is located in the frontoparietal region. En coup de sabre is a unique localized scleroderma which affects children or young adults and is usually diagnosed before the child attains 18 years of age. En coup de sabre develops suddenly in the form of plaque or scar like band on the scalp or along the line of a limb. However it can affect anyone of any age or gender. There can be multiple lesions of linear scleroderma present at a time. The differentiating feature in Morphea and En coup de sabre is that the skin in the former one is localized but the skin in the later one is fixed to underlying tissue. Although the calcinosis can be seen in this condition rarely. The serological abnormalities found in this condition are rheumatoid factor, anti-single stranded DNA antibodies, and anti nuclear antibodies.
DIFFERENTIATION FROM SYSTEMIC SCLERODERMA
Linear scleroderma is differentiated from systemic scleroderma on the basis of below listed points:
- Absence of Acrosclerosis
- Absence of Raynaud's phenomenon
- Absence of systemic organ involvement
- Prognosis in Linear scleroderma is better as compared to systemic sclerosis
PATHOPHYSIOLOGY
In Linear scleroderma the main finding observed is endothelial cell injury and profibrogenic pathway upregulation. In the long term it can be associated with dementia, epilepsy, and neurological deficit.
SIGNS AND SYMPTOMS
- Skin discoloration
- Band like sclerotic lesion
- Band not extending below the eyebrow
- Atrophy of skin and muscles
- In some cases atrophy of bone is also seen
- Ophthalmological involvement like ptosis of eye
- Facial asymmetry
- Facial hemiatrophy
- Facial palsy
DIAGNOSIS
Diagnosis of En coup de sabre can be done on the basis of deep skin biopsy, ophthalmological investigations, CT scan and MRI.
TREATMENT
Specific treatment for Linear scleroderma or En coup de sabre is not found yet in modern medicine system and the treatment is done symptomatically. Treatment may include tropical and oral steroids, surgical intervention for bone reconstruction, and physiotherapy.
AYURVEDIC TREATMENT FOR EN COUP DE SABRE
Ayurveda is the ancient Indian system of medicine which is now practiced and used for the treatment of various diseases worldwide. As per Ayurveda there is vitiatation of three different doshas involved in various diseases. Scleroderma is compared here with the Vata rakta. Treatment for it is also based on a similar pattern. Medicines are prescribed on the basis of similar Vata and rakta pacifying herbs. Other than herbs courses of Vamana and Virechana also have healing effects on Scleroderma.
TREATMENT OFFERED BY PLANET AYURVEDA
Planet Ayurveda is a renowned herbal company offering treatment for various diseases. All the medicines manufactured and prescribed are prepared pure and standardized from the best quality of herbs. Here for En coup de sabre Planet Ayurveda offers a Sclero Care Pack. It consists of various herbal remedies prepared from herbs that specifically act on pathophysiology of this disease.
PRODUCTS LIST
Sclero Care Pack Includes:
- Gotu Kola Capsules
- Sanjivani Vati
- Boswellia Curcumin
- Ashwagandha Capsules
- Gandhak Rasayan
- Sinhnaad Guggul
Sclero Care Pack
PRODUCTS DESCRIPTION
1. Ashwagandha Capsules
These herbal capsules are prepared from standardized extract of Ashwagandha (Withania somnifera). It has immunomodulatory properties and also provides strength to the body as a whole. It balances the tri dosha in the body and eliminates toxins from the body.
Dosage: 1 capsule twice daily with warm water.
2. Boswellia Curcumin
They are made from standardized extract of two herbs, i.e. Sallaki (Boswellia serrata) and Curcumin (Curcuma longa). Sallaki poses anti-inflammatory properties and Curcumin contains anti inflammatory, anti bacterial, anti fungal and anti cancer properties. It also relieves pain.
Dosage: 2 capsules twice daily with warm water.
3. Gotu Kola Capsules
It is prepared from pure extract of herb Gotukola (Centella asiatica). These herbal capsules promote healthy metabolism, blood circulation, combats stress, fatigue and anxiety.
Dosage:2 capsules twice daily with warm water.
4. Gandhak Rasayan
These herbal tablets consist of purified sulphur, i.e. shuddh gandhak. Gandhak rasayan helps in maintaining healthy skin and helps in treating various skin problems. It also fights against infections and treats inflammation. Gandhak rasayan is a strong herbal blood purifier.
Dosage: 2 tablets twice daily with warm water.
5. Sanjivani Vati
It is a poly herbal remedy, consisting of various herbs like Vidanga, Sonth, Pippali, Haritaki, Amalaki, Vacha, etc. These herbal tablets help in managing Vata and Pitta dosha in the body. Sanjivani vati other than possessing anti inflammatory properties also acts as toxin cleanser for the body.
Dosage: 2 tablets twice daily with warm water.
6. Sinhnaad Guggul
It is a classical Herbal formulation. It is prepared from the herbs like Triphala (Three myrobalans), shuddha gandhak (Purified sulphur), shuddha guggul (Purified Commiphora mukul) and Eranda taila (oil of Ricinus communis).
Dosage : 2 tablets twice daily with warm water.
CONCLUSION
En coup de sabre is a rare disease affecting the people in the first or second decade of their life. With the help of Sclero care pack this complex and difficult to treat disease can be managed and treated successfully also patients can have better quality of life with these herbal medicines without having any side effects even when taken for long term.
No comments:
Post a Comment